Pathways of ammonia detoxification to GLN in muscles connected to Improved use in the BCAA and ?-KG (cataplerosis) and recommended outcomes of BCAA and phenylbutyrate in topics with liver cirrhosis or UCD. Good result of BCAA on ammonia detoxification to GLN may very well be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbu